Polycystic Kidney Disease Types: Autosomal Recessive
Autosomal recessive
polycystic kidney disease is a rare form of PKD that usually causes symptoms in early childhood, even in the womb. It is estimated to occur in 1 in every 20,000 to 40,000 people.
Autosomal recessive PKD symptoms can begin before birth, so it is often called "infantile PKD." Children born with autosomal recessive PKD usually develop kidney failure within a few years. The severity of the disease varies. Babies with the worst cases die hours or days after birth. Children with an infantile form of autosomal recessive PKD may have sufficient kidney function for normal activities for a few years. People with juvenile PKD may live into their teens or twenties, and usually will have liver problems as well.
Polycystic Kidney Disease Types: Acquired Cystic Kidney Disease
Acquired cystic kidney disease (ACKD) develops in kidneys with long-term damage and bad scarring, so it is often associated with dialysis and end-stage renal disease. About 90 percent of people who have been on dialysis for five years develop ACKD. People with ACKD can have any underlying kidney disease, such as glomerulonephritis (kidney disease from
diabetes).
The cysts of ACKD may bleed. Kidney tumors, including kidney (renal) cancer, can develop in people with ACKD. Renal cancer is rare, yet occurs at least twice as often in ACKD patients as in the general population.
Acquired cystic kidney disease is not an inherited form of PKD.
Previous
Add this article to your Favorites
Email this article
Print